Cystic temporofacial rhabdomyosarcoma with subarachnoid communication.

Rhabdomyosarcoma (RMS) is the most common soft-tissue sarcoma of childhood. The neoplasm probably originates from pluripotential mesenchyme, and may occur anywhere in the body. Thirty to 40% arise in the head and neck. Imaging studies typically show a homogeneous soft-tissue mass, often with poorly defined margins and permeative bone destruction (1-5). We report an unusual case of embryonal RMS of the facial soft tissues. The tumor consisted of a cavity with multiple extensions that communicated with the subarachnoid space.